Abstract
Marfan syndrome is the most prevalent connective tissue disorder, with an autosomal dominant inheritance with variable penetrance. This paper aims to summarize epidemiology and treatment for type B dissection in Marfan patients.
MeSH terms
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Animals
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Aortic Aneurysm / diagnosis
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Aortic Aneurysm / epidemiology*
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Aortic Aneurysm / surgery
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Aortic Dissection / diagnosis
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Aortic Dissection / epidemiology*
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Aortic Dissection / surgery
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Blood Vessel Prosthesis Implantation
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Diagnostic Imaging / methods
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Endovascular Procedures
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Genetic Predisposition to Disease
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Humans
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Marfan Syndrome / diagnosis
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Marfan Syndrome / epidemiology*
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Marfan Syndrome / genetics
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Phenotype
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Predictive Value of Tests
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Prevalence
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Risk Factors
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Treatment Outcome