The risk for type B aortic dissection in Marfan syndrome

J Cardiovasc Surg (Torino). 2015 Dec;56(6):899-904. Epub 2015 Sep 8.

Abstract

Marfan syndrome is the most prevalent connective tissue disorder, with an autosomal dominant inheritance with variable penetrance. This paper aims to summarize epidemiology and treatment for type B dissection in Marfan patients.

Publication types

  • Review

MeSH terms

  • Animals
  • Aortic Aneurysm / diagnosis
  • Aortic Aneurysm / epidemiology*
  • Aortic Aneurysm / surgery
  • Aortic Dissection / diagnosis
  • Aortic Dissection / epidemiology*
  • Aortic Dissection / surgery
  • Blood Vessel Prosthesis Implantation
  • Diagnostic Imaging / methods
  • Endovascular Procedures
  • Genetic Predisposition to Disease
  • Humans
  • Marfan Syndrome / diagnosis
  • Marfan Syndrome / epidemiology*
  • Marfan Syndrome / genetics
  • Phenotype
  • Predictive Value of Tests
  • Prevalence
  • Risk Factors
  • Treatment Outcome