No abstract available
Keywords:
4-phenylbutyrate; epidermolysis bullosa simplex; keratin aggregates; trimethylamine N-oxide.
Publication types
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Letter
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Research Support, Non-U.S. Gov't
MeSH terms
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Cytoskeleton / metabolism
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Epidermolysis Bullosa Simplex / metabolism*
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HSP40 Heat-Shock Proteins / metabolism
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HSP70 Heat-Shock Proteins / metabolism
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Hot Temperature
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Humans
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Keratinocytes / cytology*
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Keratins / genetics*
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Keratins / metabolism*
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Methylamines / chemistry*
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Molecular Chaperones / metabolism
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Mutation
Substances
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HSP40 Heat-Shock Proteins
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HSP70 Heat-Shock Proteins
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Methylamines
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Molecular Chaperones
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Keratins
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trimethyloxamine