Diffuse intra-abdominal low grade fibromyxoid sarcoma with hepatic metastases: Case report and review of the literature

Jana Konecna; Gabriel Liberale; Johnny Haddad; Nicolas de Saint-Aubain; Issam El Nakadi

doi:10.1016/j.ijscr.2015.06.022

Diffuse intra-abdominal low grade fibromyxoid sarcoma with hepatic metastases: Case report and review of the literature

Int J Surg Case Rep. 2015:14:40-3. doi: 10.1016/j.ijscr.2015.06.022. Epub 2015 Jul 15.

Authors

Jana Konecna¹, Gabriel Liberale², Johnny Haddad¹, Nicolas de Saint-Aubain³, Issam El Nakadi¹

Affiliations

¹ Department of Digestive Surgery, Institut Jules Bordet, Brussels, Belgium.
² Department of Digestive Surgery, Institut Jules Bordet, Brussels, Belgium. Electronic address: gabriel.liberale@bordet.be.
³ Department of Pathological Anatomy, Institut Jules Bordet, Brussels, Belgium.

Abstract

Introduction: Low grade fibromyxoid sarcoma (LGFMS)(1) is a rare soft tissue tumor involving deep soft tissues of the extremities and trunk. Abdominal location is extremely uncommon in which the few cases published in the literature are characterized by slow tumoral progression and long recurrence-free intervals.

Methods: We report the first case of an intra-abdominal LGFMS which was discovered incidentally in a 42-year-old woman presenting diffuse peritoneal nodules and hepatic metastasis on CT and MRI scans.

Results: The patient was successfully treated through conservative measures and remained asymptomatic at the 48 month follow-up.

Conclusions: This is the first reported case of LGFMS with peritoneal and hepatic metastases. Despite the discovery of an advance disease at exploration, the patient who refused a major surgical operation presents an uneventful follow-up and long term survival.

Keywords: Hepatic metastases; Low grade fibromyxoid sarcoma; Peritoneal metastases; Prognosis; Treatment.