Cutaneous sarcoidosis simulating porokeratosis of Mibelli

Pan Afr Med J. 2015 Mar 3:20:195. doi: 10.11604/pamj.2015.20.195.5003. eCollection 2015.

Abstract

We report a skin localization of systemic sarcoidosis, which presented with lesions that resemble porokeratosis of Mibelli. Skin biopsy showed non-caseating sarcoidal granuloma. Whereas cutaneous sarcoidosis is present in up to one-third of cases and may present with a wide variety of lesions, our presentation is uncommon. Partial remission was obtained with hydroxychloroquine and prednisone.

Keywords: Sarcoidosis; granuloma; porokeratosis of Mibelli.

Publication types

  • Case Reports

MeSH terms

  • Anti-Inflammatory Agents / administration & dosage
  • Anti-Inflammatory Agents / therapeutic use
  • Biopsy
  • Humans
  • Hydroxychloroquine / administration & dosage
  • Hydroxychloroquine / therapeutic use
  • Male
  • Middle Aged
  • Porokeratosis / diagnosis*
  • Porokeratosis / pathology
  • Prednisone / administration & dosage
  • Prednisone / therapeutic use
  • Remission Induction / methods
  • Sarcoidosis / diagnosis*
  • Sarcoidosis / drug therapy
  • Sarcoidosis / pathology
  • Skin Diseases / diagnosis*
  • Skin Diseases / drug therapy
  • Skin Diseases / pathology

Substances

  • Anti-Inflammatory Agents
  • Hydroxychloroquine
  • Prednisone