Melanocytoma, a specific variant of melanocytic naevus may occur anywhere along the uveal tract but most commonly it is on the optic disk and adjacent choroid. We report a case of necrotic melanocytoma with associated polycystic liver disease and peripheral neurofibromatosis in a 70-year old man who was referred to the eye unit of the Korle bu Teaching hospital, Accra, Ghana with a CT scan suggestive of choroidal melanoma. Histopathological features of the enucleated eye revealed necrotic melanocytoma. He also had other systemic conditions. The case is presented and the literature reviewed.
Keywords: Accra; Ghana; Necrotic melanocytoma; Neurofibromatosis; Polycystic liver.