Postpartum pulmonary embolism in a patient with Fontan circulation

World J Pediatr Congenit Heart Surg. 2015 Apr;6(2):317-9. doi: 10.1177/2150135114568786.

Abstract

Pregnancy is typically not recommended in patients with Fontan circulation. Although patients are well aware of the risks for the mother and fetus, an increasing number opt to become pregnant. The higher rate of survival into adulthood post-Fontan procedure is a likely factor as a result of improved management of single ventricle anatomy. Postpartum thromboembolism is a known complication, but its prevalence and management are not clearly defined. We present a case of massive pulmonary embolism two weeks postpartum in a patient with double inlet left ventricle palliated with lateral tunnel Fontan.

Keywords: Fontan procedure; postpartum; pregnancy; pulmonary embolectomy; pulmonary embolism; thromboprophylaxis.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Diagnosis, Differential
  • Female
  • Fontan Procedure*
  • Heart Defects, Congenital*
  • Humans
  • Infant, Newborn
  • Postpartum Period
  • Pregnancy
  • Pregnancy Complications, Cardiovascular*
  • Pulmonary Embolism / diagnosis*
  • Pulmonary Embolism / diagnostic imaging
  • Radiography