Refractory cardiogenic shock in a patient with β-thalassemia major requiring mechanical circulatory support: Case report and literature review

Pediatr Transplant. 2015 Jun;19(4):E93-6. doi: 10.1111/petr.12454. Epub 2015 Mar 11.

Abstract

Iron overload cardiomyopathy secondary to β-thalassemia major is a potentially reversible condition managed with chelation and medical hemodynamic support, as bridge-to-recovery or transplant. We describe our experience, and challenges faced, in a pediatric patient with iron overload cardiomyopathy secondary to β-thalassemia major, requiring biventricular MCS.

Keywords: cardiomyopathy; paediatrics; surgery; transition.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Adolescent
  • Cardiomyopathies / etiology
  • Cardiomyopathies / therapy
  • Chelating Agents / therapeutic use
  • Female
  • Heart Transplantation
  • Heart-Assist Devices / statistics & numerical data
  • Hemodynamics
  • Humans
  • Iron Overload / etiology
  • Iron Overload / therapy
  • Radiography, Thoracic
  • Shock, Cardiogenic / etiology*
  • Shock, Cardiogenic / therapy
  • beta-Thalassemia / complications
  • beta-Thalassemia / therapy*

Substances

  • Chelating Agents