Laparoscopic reconstruction of an iatrogenic perforation of the neovagina and urinary bladder by a neovaginal dilator in a patient with Mayer-Rokitansky-Küster-Hauser syndrome

Int Urogynecol J. 2015 Jul;26(7):1083-7. doi: 10.1007/s00192-014-2609-1. Epub 2015 Jan 15.

Abstract

Introduction and hypothesis: Mayer-Rokitansky-Küster-Hauser syndrome (MRKH) is a rare genital aplasia syndrome. Patients with MRKH regularly dilate their neovagina with vaginal dilatators.

Methods: A 23-year-old MRKH syndrome patient came to our department complaining of a lost vaginal dilator, which she had inserted 2 days previously. She had no bleeding or abdominal pain, but did have occasional urine loss. She had a history of abdominal exploration for an acute abdomen and the creation of a neovagina at the age of 16. An abdominal CT scan located the dislocated dilator intravesically. After diagnostic laparoscopy, the dilator was removed through the vesico-neovaginal perforation. The vagina was closed and covered by a pedicled peritoneal flap, followed by closure of the urinary bladder. An omental J-flap was then fixed between the vagina and bladder.

Results: The operative time was 185 min, with no significant blood loss, injuries or need for conversion/revision. The indwelling catheter was removed 7 days later after cystography, followed by normal micturition and an adequate bladder capacity. Vaginal dilation and sexual activity was resumed 1 month postoperatively. Follow-up was uneventful.

Conclusions: Laparoscopic vaginal dilator removal with immediate repair of the perforation of the neovagina and the urinary bladder directly after an acute trauma in a patient with MRKH syndrome may be a management option. It is a feasible, safe and viable operation in the hands of experienced laparoscopists.

Publication types

  • Case Reports

MeSH terms

  • 46, XX Disorders of Sex Development*
  • Congenital Abnormalities*
  • Female
  • Gynecologic Surgical Procedures*
  • Humans
  • Iatrogenic Disease
  • Laparoscopy
  • Mullerian Ducts / abnormalities*
  • Surgically-Created Structures*
  • Urinary Bladder / injuries*
  • Urinary Bladder / surgery
  • Young Adult

Supplementary concepts

  • Mullerian aplasia