Evans Syndrome: A case report

Pediatr Med Chir. 2014 Aug 31;36(4):91. doi: 10.4081/pmc.2014.91.

Abstract

We describe a case of a 14-years old caucasian female affected by autoimmune hemolytic anemia and thrombocytopenia successfully treated with intravenous immunoglobulin and steroids. Nevertheless, neutropenia occurred during follow-up period. Positivity of direct antiglobulin test and sieric anti-neutrophil antibodies suggested the diagnosis of Evans syndrome trilineage.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Aftercare
  • Anemia, Hemolytic, Autoimmune / diagnosis*
  • Anemia, Hemolytic, Autoimmune / drug therapy
  • Antibodies, Antineutrophil Cytoplasmic / analysis
  • Coombs Test / methods
  • Female
  • Humans
  • Immunoglobulins, Intravenous / therapeutic use*
  • Neutropenia / pathology
  • Steroids / therapeutic use*
  • Thrombocytopenia / diagnosis*
  • Thrombocytopenia / drug therapy

Substances

  • Antibodies, Antineutrophil Cytoplasmic
  • Immunoglobulins, Intravenous
  • Steroids

Supplementary concepts

  • Evans Syndrome