Selective agenesis of pancreatic isthmus parenchyma with preservation of main pancreatic duct continuity, a very rare entity: Case report

Salvatore Paiella; Matteo De Pastena; Alessandro Esposito; Roberto Salvia; Consuelo Morigi; Claudio Bassi

doi:10.1016/j.ijscr.2014.09.023

Selective agenesis of pancreatic isthmus parenchyma with preservation of main pancreatic duct continuity, a very rare entity: Case report

Int J Surg Case Rep. 2015:6C:169-71. doi: 10.1016/j.ijscr.2014.09.023. Epub 2014 Dec 11.

Authors

Salvatore Paiella¹, Matteo De Pastena², Alessandro Esposito², Roberto Salvia², Consuelo Morigi², Claudio Bassi²

Affiliations

¹ University of Verona, Department of General Surgery B, Istituto del Pancreas, Verona, Italy. Electronic address: salvatore.paiella@ospedaleuniverona.it.
² University of Verona, Department of General Surgery B, Istituto del Pancreas, Verona, Italy.

Abstract

Context: Agenesis of the dorsal pancreas is a rare anomaly, mostly associated with other medical conditions. It may be complicated with pancreatic neoplasms.

Case report: We report the case of a 51-year-old male with selective agenesis of pancreatic isthmus with preservation of main pancreatic duct and branch-duct intraductal papillary mucinous neoplasm (BD-IPMN) with suspicious features of the pancreas.

Conclusion: This is probably the first report of isolated agenesis of pancreatic isthmus with conservation of main pancreatic duct.

Keywords: Agenesis of pancreatic isthmus; BD-IPMN; Dorsal pancreatic agenesis; IPMN; Pancreatic anomaly.