Correction of aortic coarctation in a girl with severe PHACE syndrome

J Cardiothorac Surg. 2014 Oct 14:9:169. doi: 10.1186/s13019-014-0169-6.

Abstract

A 12-year-old Chinese girl was demonstrated multivessel distortion and malformation: aortic coarctation with the narrowest lumen diameter measuring of 4 mm located between the left common carotid artery and the left subclavian artery, a huge and thin-walled aneurysm is connected to the coarctation, and the descending aorta was distorted. Cerebrovascular revealed distorted arteries and a completely aberrant brain blood supply. She underwent correction of the aortic coarctation by establishing a bypass between the ascending aorta and the descending aorta using a 13-mm Gore-tex tube. Postoperative recovery was uneventful, at 6-month follow-up, the cervical vascular pulsatility was relieved and she is in good condition.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Aortic Coarctation / complications
  • Aortic Coarctation / surgery*
  • Child
  • Eye Abnormalities*
  • Female
  • Humans
  • Neurocutaneous Syndromes*

Supplementary concepts

  • PHACE association