Properdin deficiency-associated bronchiectasis

Ann Allergy Asthma Immunol. 2014 Jun;112(6):557-9. doi: 10.1016/j.anai.2014.04.003. Epub 2014 May 1.
No abstract available

Publication types

  • Case Reports
  • Letter

MeSH terms

  • Adult
  • Bronchiectasis / genetics
  • Bronchiectasis / pathology*
  • Complement C3 / immunology
  • Complement Pathway, Alternative / genetics
  • Female
  • Genetic Diseases, X-Linked / genetics*
  • Genetic Diseases, X-Linked / immunology
  • Genetic Diseases, X-Linked / pathology*
  • Hereditary Complement Deficiency Diseases
  • Humans
  • Immunologic Deficiency Syndromes / genetics*
  • Immunologic Deficiency Syndromes / immunology
  • Immunologic Deficiency Syndromes / pathology*
  • Properdin / deficiency*
  • Properdin / genetics
  • Properdin / immunology

Substances

  • Complement C3
  • Properdin

Supplementary concepts

  • Properdin Deficiency, Type II