No abstract available
MeSH terms
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Adult
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Bronchiectasis / genetics
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Bronchiectasis / pathology*
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Complement C3 / immunology
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Complement Pathway, Alternative / genetics
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Female
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Genetic Diseases, X-Linked / genetics*
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Genetic Diseases, X-Linked / immunology
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Genetic Diseases, X-Linked / pathology*
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Hereditary Complement Deficiency Diseases
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Humans
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Immunologic Deficiency Syndromes / genetics*
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Immunologic Deficiency Syndromes / immunology
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Immunologic Deficiency Syndromes / pathology*
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Properdin / deficiency*
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Properdin / genetics
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Properdin / immunology
Supplementary concepts
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Properdin Deficiency, Type II