Ewing sarcoma/peripheral primitive neuroectodermal tumor in the adrenal gland of an adolescent: a case report and review of the literature

J Pediatr Hematol Oncol. 2014 Oct;36(7):e456-9. doi: 10.1097/MPH.0000000000000058.

Abstract

Ewing sarcoma/peripheral primitive neuroectodermal tumors (ES/pPNETs) typically occur in the long or flat bones, the chest wall, extraskeletal soft tissue, or less frequently, in solid organs. They can arise from anywhere in the body; however, ES/pPNETs arising from the adrenal gland are very rare, especially in children and adolescents. Herein, the authors report a case of an ES/pPNET in the adrenal gland of a 17-year-old girl, who was successfully treated with a multimodal treatment, with a brief review of the pertinent literature.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't
  • Review

MeSH terms

  • Adolescent
  • Adrenal Gland Neoplasms / diagnosis*
  • Adrenal Gland Neoplasms / therapy
  • Bone Neoplasms / diagnosis*
  • Bone Neoplasms / therapy
  • Chemoradiotherapy / methods
  • Female
  • Humans
  • Neoplasms, Second Primary / diagnosis*
  • Neoplasms, Second Primary / therapy
  • Neuroectodermal Tumors, Primitive, Peripheral / diagnosis*
  • Neuroectodermal Tumors, Primitive, Peripheral / therapy
  • Sarcoma, Ewing / diagnosis*
  • Sarcoma, Ewing / therapy