Severe mitral stenosis secondary to Hunter's syndrome

Circulation. 2013 Sep 10;128(11):1269-70. doi: 10.1161/CIRCULATIONAHA.113.001688.
No abstract available

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't
  • Video-Audio Media

MeSH terms

  • Adult
  • Amylases
  • Diagnosis, Differential
  • Dyspnea / etiology
  • Electrocardiography
  • Emergencies
  • Enzyme Replacement Therapy
  • Glycoproteins / therapeutic use
  • Glycosaminoglycans / analysis
  • Heart Valve Prosthesis Implantation
  • Humans
  • Male
  • Mitral Valve / chemistry
  • Mitral Valve / pathology
  • Mitral Valve Stenosis / diagnostic imaging
  • Mitral Valve Stenosis / etiology*
  • Mitral Valve Stenosis / physiopathology
  • Mitral Valve Stenosis / surgery
  • Mucopolysaccharidosis II / complications*
  • Mucopolysaccharidosis II / drug therapy
  • Mucopolysaccharidosis II / enzymology
  • Periodic Acid-Schiff Reaction
  • Rheumatic Heart Disease / diagnosis
  • Staining and Labeling
  • Ultrasonography

Substances

  • Glycoproteins
  • Glycosaminoglycans
  • IDS protein, human
  • Amylases