Congenital megalourethra presenting with large cystic mass in the inguinal area

Eur J Pediatr. 2014 Feb;173(2):257-8. doi: 10.1007/s00431-013-2134-0. Epub 2013 Aug 22.

Abstract

Congenital megalourethra is a rare urogenital malformation characterized by severe dilatation and elongation of the penile urethra. It causes functional obstruction of the lower urinary system. Herein, we present a newborn with congenital megalourethra with single umbilical artery.

MeSH terms

  • Cysts / congenital*
  • Groin*
  • Humans
  • Hydronephrosis / diagnosis
  • Hydronephrosis / surgery
  • Infant, Newborn
  • Male
  • Penis / abnormalities*
  • Rectal Fistula / diagnosis*
  • Rectal Fistula / surgery
  • Umbilical Arteries / abnormalities*
  • Urethra / abnormalities*
  • Urethral Diseases / diagnosis*
  • Urethral Diseases / surgery
  • Urinary Diversion
  • Urinary Fistula / diagnosis*
  • Urinary Fistula / surgery