Functional single-nucleotide variant of HSPD1 in sudden infant death syndrome

Pediatr Res. 2013 Oct;74(4):380-3. doi: 10.1038/pr.2013.112. Epub 2013 Jul 3.

Abstract

Background: An insufficient stress response due to a genetically impaired heat shock protein (Hsp) could play a role in the pathogenesis in a subgroup of sudden infant death syndrome (SIDS) cases. Herein, we are the first to investigate whether a functionally impairing and thus pathogenic variant of the gene for Hsp60, encoded by HSPD1 (rs72466451), is correlated with the occurrence of SIDS.

Methods: In a case-control study of a series of 133 cases of SIDS and 192 gender-matched German Caucasian control cases, the occurrence and distribution of the HSPD1 single-nucleotide variant (SNV) was analyzed using SNV genotyping by minisequencing.

Results: The results show significantly increased frequency of the pathogenic variant of the HSPD1 SNV in a subgroup (4.5%) of SIDS cases.

Conclusion: The results suggest that the pathogenic variant of rs72466451 may play a role in a subgroup of SIDS cases with impaired Hsp60-mediated stress response.

MeSH terms

  • Base Sequence
  • Case-Control Studies
  • Chaperonin 60 / genetics*
  • DNA Primers / genetics
  • Female
  • Gene Frequency
  • Genetic Association Studies
  • Genotype
  • Germany
  • Humans
  • Infant
  • Male
  • Mitochondrial Proteins / genetics*
  • Molecular Sequence Data
  • Polymorphism, Single Nucleotide / genetics*
  • Sequence Analysis, DNA
  • Stress, Physiological / genetics*
  • Stress, Physiological / physiology
  • Sudden Infant Death / genetics*

Substances

  • Chaperonin 60
  • DNA Primers
  • HSPD1 protein, human
  • Mitochondrial Proteins