No abstract available
MeSH terms
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1-Deoxynojirimycin / analogs & derivatives*
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1-Deoxynojirimycin / pharmacology
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1-Deoxynojirimycin / therapeutic use
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Animals
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Calcium / metabolism
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Clinical Trials as Topic
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Disease Models, Animal
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Enzyme Inhibitors / pharmacology*
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Enzyme Inhibitors / therapeutic use*
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Glucosyltransferases / antagonists & inhibitors
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Humans
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Lysosomes / metabolism
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Mice
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Niemann-Pick Disease, Type C / drug therapy*
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Niemann-Pick Disease, Type C / physiopathology
Substances
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Enzyme Inhibitors
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1-Deoxynojirimycin
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miglustat
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Glucosyltransferases
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ceramide glucosyltransferase
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Calcium