[Primary retroperitoneal fibrosis: a report of 7 cases]

Rev Med Liege. 2012 Jul-Aug;67(7-8):425-9.
[Article in French]

Abstract

Retroperitoneal fibrosis is a rare fibrosing disease of the retroperitoneal tissue characterized by a significant clinico-biological polymorphism. No codified treatment exists, particularly for the primary type which is the most frequent. We retrospectively report on 7 cases of primary retroperitoneal fibrosis seen over a period of 10 years. There were 4 men and 3 women (mean age: 58 years).The most common presenting symptom was lumbar pain. A biological inflammatory syndrome and a renal insufficiency were found in 4 cases. The diagnosis was confirmed by abdominal CT scan and/or histology. Etiological investigations remained negative. The evolution was generally favourable under corticosteroids. Retroperitoneal fibrosis requires a careful etiological investigation before it is considered primary. Prognosis is good in spite of the absence of a well codified treatment.

Publication types

  • English Abstract

MeSH terms

  • Adult
  • Aged
  • Diagnostic Imaging
  • Female
  • Glucocorticoids / therapeutic use
  • Humans
  • Low Back Pain / etiology
  • Male
  • Middle Aged
  • Prednisone / therapeutic use
  • Retroperitoneal Fibrosis / diagnosis*
  • Retroperitoneal Fibrosis / drug therapy*
  • Retrospective Studies

Substances

  • Glucocorticoids
  • Prednisone