Tetralogy of Fallot with cor triatriatum dexter in an adult patient: a case report

Congenit Heart Dis. 2013 May-Jun;8(3):E77-80. doi: 10.1111/j.1747-0803.2012.00671.x. Epub 2012 May 22.

Abstract

Tetralogy of Fallot (TOF) is the most common cyanotic congenital heart defect with only approximately 3% of uncorrected patients surviving past age 40. In this case report, we present a 48-year-old mentally retarded man suffering from congenital spastic quadriplegia who was diagnosed with a unique combination of symptomatic TOF and cor triatriatum dexter (CTD). Reduced preload because of CTD with spastic quadriplegia that prevented physical exertion is believed to have facilitated this patient's unusually long survival.

Publication types

  • Case Reports

MeSH terms

  • Appendectomy / adverse effects
  • Cor Triatriatum / complications*
  • Cor Triatriatum / diagnosis
  • Cor Triatriatum / physiopathology
  • Disease Progression
  • Echocardiography, Doppler
  • Fatal Outcome
  • Heart Failure / etiology
  • Hemodynamics
  • Humans
  • Intellectual Disability / complications
  • Male
  • Middle Aged
  • Physical Exertion
  • Quadriplegia / complications
  • Tetralogy of Fallot / complications*
  • Tetralogy of Fallot / diagnosis
  • Tetralogy of Fallot / physiopathology
  • Time Factors