Neurofibromatosis 2

Otolaryngol Clin North Am. 2012 Apr;45(2):315-32, viii. doi: 10.1016/j.otc.2011.12.005.

Abstract

A comprehensive discussion of neurofibromatosis 2 (NF2) is presented, including clinical characteristics, symptoms, diagnosis, tumor types, prevalence and incidence, genetic testing, imaging, treatment options, and follow-up management of NF2.

Publication types

  • Review

MeSH terms

  • Cranial Nerve Neoplasms / diagnosis
  • Cranial Nerve Neoplasms / epidemiology
  • Diagnosis, Differential
  • Diagnostic Imaging / methods
  • Eye Abnormalities / diagnosis
  • Eye Abnormalities / epidemiology
  • Female
  • Genes, Neurofibromatosis 2*
  • Genetic Predisposition to Disease / epidemiology*
  • Humans
  • Incidence
  • Male
  • Meningioma / diagnosis
  • Meningioma / epidemiology
  • Neurofibromatosis 1 / diagnosis*
  • Neurofibromatosis 1 / epidemiology
  • Neurofibromatosis 1 / therapy
  • Neurofibromatosis 2 / diagnosis*
  • Neurofibromatosis 2 / epidemiology*
  • Neurofibromatosis 2 / genetics
  • Neurofibromatosis 2 / therapy
  • Neuroma, Acoustic / diagnosis
  • Neuroma, Acoustic / epidemiology
  • Prognosis
  • Risk Assessment
  • Spinal Neoplasms / diagnosis
  • Spinal Neoplasms / epidemiology
  • Survival Analysis