Multiple dysplastic liver nodules in PFIC2 underscore risk for neoplasia associated with functional BSEP deficiency

Am J Surg Pathol. 2012 May;36(5):785-6. doi: 10.1097/PAS.0b013e3182500c35.
No abstract available

Publication types

  • Case Reports
  • Letter

MeSH terms

  • ATP Binding Cassette Transporter, Subfamily B, Member 11
  • ATP-Binding Cassette Transporters / genetics
  • ATP-Binding Cassette Transporters / metabolism*
  • Adolescent
  • Biomarkers / metabolism
  • Cholestasis, Intrahepatic / complications
  • Cholestasis, Intrahepatic / diagnosis*
  • Cholestasis, Intrahepatic / genetics
  • Cholestasis, Intrahepatic / metabolism
  • Genetic Markers
  • Humans
  • Liver Neoplasms / complications
  • Liver Neoplasms / diagnosis*
  • Liver Neoplasms / genetics
  • Liver Neoplasms / metabolism
  • Risk

Substances

  • ABCB11 protein, human
  • ATP Binding Cassette Transporter, Subfamily B, Member 11
  • ATP-Binding Cassette Transporters
  • Biomarkers
  • Genetic Markers

Supplementary concepts

  • Cholestasis, progressive familial intrahepatic 2