Congenital microgastria with limb defect combined with megaduodenum: case report and review of literature

Indian J Surg. 2011 Apr;73(2):122-4. doi: 10.1007/s12262-010-0185-2. Epub 2010 Nov 30.

Abstract

Congenital microgastria is a rare developmental disorder with only 59 previously reported cases. Most of the patients undergoing reconstructive surgery are in early infancy, providing gastric augmentation to achieve optimal thrive. The Hunt-Lawrence pouch is the standard surgical treatment in infancy, but late surgery in early adulthood requires different approach. This case demonstrates that duodenojejunostomy is safe and effective in the treatment of congenital, functional duodenal obstruction in adulthood.

Keywords: Developmental abnormality; Duodeno- jejunal bypass; Hunt-Lawrence pouch; Limb defect; Microgastria.