Adult-onset cerebral folate deficiency

Arch Neurol. 2012 Jun;69(6):778-9. doi: 10.1001/archneurol.2011.3036.

Abstract

Objective: To report new manifestations of cerebral folate deficiency, a rare metabolic autoimmune syndrome,in an adult.

Design: Case report.

Setting: University teaching hospital.

Patient: A 58-year-old woman with progressive memory loss and myoclonus presented for medical attention. Results of cerebral spinal fluid analysis showed low levels of tetrahydrobiopterin and 5-methyltetrahydrofolate. The patient's serum folate level was normal. Serum contained folate receptor 1 blocking and binding antibodies.

Results: The patient was treated successfully with folinic acid supplementation, and after 6 months of treatment,clinical symptoms had resolved.

Conclusions: To our knowledge, we report the first case of adult-onset cerebral folate deficiency. Furthermore, this condition could represent a treatable form of early-onset dementia.

Publication types

  • Case Reports

MeSH terms

  • Brain Diseases / complications*
  • Brain Diseases / diet therapy
  • Brain Diseases / pathology*
  • Cerebral Cortex / pathology*
  • Female
  • Humans
  • Leucovorin / administration & dosage
  • Middle Aged
  • Vitamin B Deficiency / complications*
  • Vitamin B Deficiency / diet therapy

Substances

  • Leucovorin