[Adrenal pheochromocytoma with multiple neurofibromatosis on the trunk]

Hinyokika Kiyo. 2012 Jan;58(1):17-9.
[Article in Japanese]

Abstract

We report a case of adrenal pheochromocytoma in a patient with neurofibromatosis type 1 (NF1). A 65-year-old female patient was admitted to our hospital for examination of a right adrenal mass. The adrenal tumor was incidentally discovered by abdominal computed tomography during examination for hypertension in another hospital. She had large multiple neurofibromatous lesions and café-au-lait spots on the trunk. We thought that it was difficult to make a skin incision on normal skin. Serum and urinary catecholamines were markedly increased. Magnetic resonance imaging revealed a solid round tumor 3 cm in diameter, located in the right adrenal gland. Laparoscopic right adrenalectomy was performed. Serum and urinary catecholamines returned to the normal range on post-operative day 10. Laparoscopic surgery may be a good option for NF1 patients with pheochromocytoma, especially those who had multiple neurofibromatosis on the trunk.

Publication types

  • Case Reports
  • English Abstract

MeSH terms

  • Adrenal Gland Neoplasms / complications*
  • Adrenal Gland Neoplasms / pathology
  • Adrenal Gland Neoplasms / surgery
  • Adrenalectomy
  • Aged
  • Catecholamines / analysis
  • Female
  • Humans
  • Laparoscopy
  • Magnetic Resonance Imaging
  • Neurofibromatosis 1 / complications*
  • Pheochromocytoma / complications*
  • Pheochromocytoma / pathology
  • Pheochromocytoma / surgery

Substances

  • Catecholamines