Malignant hemangiopericytoma of the condyle

J Craniofac Surg. 2012 Jan;23(1):e33-6. doi: 10.1097/SCS.0b013e318241db73.

Abstract

Hemangiopericytoma (HPC) is an uncommon vascular tumor arising from pericytic cells with variable malignant potential. Primary HPCs of the bone are extremely rare; however, involvement of the condylar process has not been reported. We presented a 21-year-old female patient with low-grade malignant HPC in the right mandibular condyle. Clinical examination and imaging findings revealed a well-defined soft mass, encapsulating the mandibular condyle from behind. The lesion and mandibular condyle were removed simultaneously; then, the costochondral graft was used to reconstruct the defect. Histopathologic examinations of the specimen confirmed the diagnosis. After 2 years of follow-up, the patient is free of disease, and mouth opening returned to normal.

Publication types

  • Case Reports

MeSH terms

  • 12E7 Antigen
  • Antigens, CD / analysis
  • Cell Adhesion Molecules / analysis
  • Diagnosis, Differential
  • Female
  • Follow-Up Studies
  • Hemangiopericytoma / diagnosis*
  • Humans
  • Magnetic Resonance Imaging
  • Mandibular Condyle / pathology*
  • Mandibular Neoplasms / diagnosis*
  • Osteotomy / methods
  • Range of Motion, Articular / physiology
  • Tomography, X-Ray Computed
  • Vimentin / analysis
  • Young Adult

Substances

  • 12E7 Antigen
  • Antigens, CD
  • CD99 protein, human
  • Cell Adhesion Molecules
  • Vimentin