Oral extragonadal yolk sac tumor in a patient with Aicardi syndrome: putative origin and differential diagnosis

Hum Pathol. 2012 Jun;43(6):939-42. doi: 10.1016/j.humpath.2011.09.015. Epub 2012 Jan 4.

Abstract

We report, for the first time, a primary oral presentation of a germ cell yolk sac tumor in a 4-year-old girl with Aicardi syndrome. The diagnosis, differential diagnosis, and histogenesis are discussed.

Publication types

  • Case Reports

MeSH terms

  • Aicardi Syndrome / complications*
  • Antineoplastic Combined Chemotherapy Protocols / therapeutic use
  • Child, Preschool
  • Diagnosis, Differential
  • Endodermal Sinus Tumor / complications*
  • Endodermal Sinus Tumor / drug therapy
  • Endodermal Sinus Tumor / pathology*
  • Female
  • Humans
  • Mouth Neoplasms / complications*
  • Mouth Neoplasms / drug therapy
  • Mouth Neoplasms / pathology*