Progressive lymphangiomatosis and Gorham's disease: case report and clinical implications

Lymphat Res Biol. 2011;9(4):201-4. doi: 10.1089/lrb.2011.0021.

Abstract

Lymphangiomatosis is a rare proliferative disorder of the lymphatic system. The etiology is unknown, rendering it difficult to manage. This case report of lymphangiomatosis with features of Gorham's disease reveals the progressive and unexpected nature of the condition. It highlights the need for further research into the pathophysiology and management of lymphangiomatosis as current treatment options are limited.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Antibiotics, Antineoplastic / therapeutic use
  • Child, Preschool
  • Diagnosis, Differential
  • Disease Progression*
  • Female
  • Humans
  • Lymphatic Vessels* / abnormalities
  • Lymphatic Vessels* / pathology
  • Lymphoproliferative Disorders / complications
  • Lymphoproliferative Disorders / diagnosis*
  • Lymphoproliferative Disorders / drug therapy
  • Osteolysis, Essential / complications
  • Osteolysis, Essential / diagnosis*
  • Osteolysis, Essential / drug therapy
  • Sirolimus / therapeutic use
  • Watchful Waiting

Substances

  • Antibiotics, Antineoplastic
  • Sirolimus