A case of severe dysmelia of all extremities

Fetal Pediatr Pathol. 2011;30(6):375-9. doi: 10.3109/15513815.2011.587496. Epub 2011 Aug 24.

Abstract

A group of limb reduction defects is defined by congenital absence of either part of limbs. We report an extremely rare case of symmetrical upper limb peromelia (absence of distal bones) and asymmetrical lower limb phocomelia (absence of long bones and a flipper-like appearance of feet) in a female fetus at the 20th week of pregnancy. No other malformations were identified. The prevalence of peromelia and phocomelia is extremely rare, and these malformations can be associated with some candidate genes (e.g. de novo apparently balanced reciprocal translocation 46,XX,t(2;12)(p25.1;q24.1)).

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Ectromelia / diagnostic imaging
  • Ectromelia / pathology
  • Female
  • Humans
  • Limb Deformities, Congenital / diagnostic imaging
  • Limb Deformities, Congenital / genetics
  • Limb Deformities, Congenital / pathology*
  • Lower Extremity Deformities, Congenital / diagnostic imaging
  • Lower Extremity Deformities, Congenital / pathology
  • Pregnancy
  • Ultrasonography, Prenatal
  • Upper Extremity Deformities, Congenital / diagnostic imaging
  • Upper Extremity Deformities, Congenital / pathology
  • Young Adult