Background: The pigmented or melanotic variant of choroid plexus carcinoma is very rarely encountered.
Case report: We report herein a case of melanotic or pigmented choroid plexus carcinoma in the posterior fossa of an 11-year-old female.
Conclusions: A histopathological study supported by immunohistochemistry helped the authors to diagnose this rare entity. How to differentiate this tumor from pigmented papillary medulloblastoma, cerebellar papillary ependymoma, and metastatic malignant melanoma is discussed.
Keywords: HMB-45; choroid plexus carcinoma; melanin; posterior fossa.