[Granulocytic sarcoma of the maxillary sinus: a pediatric case report]

Tunis Med. 2011 Mar;89(3):305-8.
[Article in French]

Abstract

Background: Granulocytic sarcoma is a rare malignant extramedullary neoplasm of myeloid precursor cells, occuring before or after onset of leukaemia. Involvement of the head and neck region is rare, generally concerning the orbit.

Aim: To illustrate imaging findings of granulocytic sarcoma in an unusual location; maxillary sinus.

Case: We report a case of maxillary sinus granulocytic sarcoma in a 13-month old boy revealed by facial nerve palsy, ptosis and jugal swelling, without any evidence of haematological disorders. The patient underwent computed tomography and magnetic resonance imaging exam which demonstrated a non specific maxillary sinus mass with destruction of the orbit floor and the alveolar bone. Diagnosis was obtained after bone biopsy allowing histological and immunohistochemical studies.

Conclusion: Granulocytic sarcoma is a serious condition because of the associated hematologic disorders. In a sinus or orbit location, imaging features are non specific. Unless hematologic history is present, diagnosis is difficult and an immuno histo chemical study is required.

Publication types

  • Case Reports
  • English Abstract

MeSH terms

  • Humans
  • Infant
  • Magnetic Resonance Imaging
  • Male
  • Maxillary Sinus*
  • Sarcoma, Myeloid / diagnosis*
  • Tomography, X-Ray Computed