Prelamin A processing and functional effects in restrictive dermopathy

Cell Cycle. 2010 Dec 1;9(23):4766-8. doi: 10.4161/cc.9.23.14210. Epub 2010 Dec 1.
No abstract available

Publication types

  • Letter
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Amino Acid Motifs
  • Cell Line
  • Cell Nucleus / metabolism
  • Contracture / metabolism
  • Fibroblasts / metabolism
  • Humans
  • Lamin Type A
  • Laminin / physiology
  • Membrane Proteins / genetics
  • Membrane Proteins / metabolism
  • Metalloendopeptidases / genetics
  • Metalloendopeptidases / metabolism
  • Nuclear Proteins / chemistry
  • Nuclear Proteins / metabolism*
  • Nuclear Proteins / physiology
  • Protein Precursors / chemistry
  • Protein Precursors / metabolism*
  • Protein Precursors / physiology
  • Protein Prenylation
  • Protein Structure, Tertiary
  • Skin Abnormalities / metabolism

Substances

  • Lamin Type A
  • Laminin
  • Membrane Proteins
  • Nuclear Proteins
  • Protein Precursors
  • prelamin A
  • Metalloendopeptidases
  • ZMPSTE24 protein, human

Supplementary concepts

  • Tight skin contracture syndrome, lethal