Mammoth orbitofrontal neurofibromatosis with herniating meningo-encephalocele

Indian J Plast Surg. 2010 Jan;43(1):81-3. doi: 10.4103/0970-0358.63957.

Abstract

We are presenting a mammoth orbito-frontal neurofibroma with a herniating meningo-encephalocele in a 23 year old African male. The tumour measured 87cm x 54cm and occupied the right orbito-temporo-facial region and had destroyed the right orbit. A pre operative embolization of the feeding vessels was followed by a one stage near total excision of the tumour and repair of the meningo-encephalocele in hypotensive anaesthesia. The excised tumour weighed 8 Kg and, to the best of our knowledge, is the largest orbito-facial neurofibroma reported in literature.

Keywords: Orbital tumour; orbital neurofi broma; orbito-frontal neurofi broma.

Publication types

  • Case Reports