Hypoparathyroidism is a cause of the tetany in children. Except from the signs of generalized neuromuscular irritability it can also present with less characteristic signs of psychomotor development retardation, calcifications in the soft tissues, including CNS. In our report we describe a case of 8-year-old boy in whom hypoparathyroidism revealed for the first time as an episode of seizures and calcifications of the basal ganglia.