Angiocentric glioma (AG) was recognized as a distinct clinicopathological tumor in 2007, but it is rarely reported. We report a patient with AG who presented with dizziness, and whose MRI images revealed a circumscribed lesion with heterogeneous contrast enhancement and evidence of previous bleeding. Thirty-three patients with AG have been reported to date. Most AG patients present with intractable seizures, usually in childhood and as young adults. However, the presentations reported are diverse, therefore the final diagnosis of AG should depend on the histopathological examination.