[Sjögren-associated MALT-type lymphoma of labial salivary glands: rare constellation with amyloidosis and IgM-paraproteinemia]

Pathologe. 2009 Nov;30(6):442-5. doi: 10.1007/s00292-009-1207-3.
[Article in German]

Abstract

We report a complex and rare combination of clinical and histological findings in a 59-year-old female patient: severe sicca-syndrome due to M. Sjögren, marginal zone B-cell lymphoma (MALT-type) in labial salivary glands with localized amyloid deposition, IgM-paraproteinemia, and Bence-Jones proteinuria. The causal association of these findings could only be elucidated by intense interdisciplinary correlation of all findings.

Publication types

  • Case Reports
  • English Abstract

MeSH terms

  • Amyloidosis / diagnosis*
  • Amyloidosis / pathology*
  • Bence Jones Protein / analysis
  • Biopsy
  • Cooperative Behavior
  • Female
  • Humans
  • Immunoglobulin M / analysis*
  • Interdisciplinary Communication
  • Lip Diseases / diagnosis*
  • Lip Diseases / pathology*
  • Lip Neoplasms / diagnosis*
  • Lip Neoplasms / pathology*
  • Lip Neoplasms / surgery
  • Lymphoma, B-Cell, Marginal Zone / diagnosis*
  • Lymphoma, B-Cell, Marginal Zone / pathology*
  • Magnetic Resonance Imaging
  • Melanoma / surgery
  • Middle Aged
  • Neoplasms, Multiple Primary / surgery
  • Paraproteinemias / diagnosis*
  • Paraproteinemias / pathology*
  • Patient Care Team
  • Postoperative Complications / diagnosis
  • Postoperative Complications / pathology
  • Salivary Gland Neoplasms / diagnosis*
  • Salivary Gland Neoplasms / pathology*
  • Salivary Glands, Minor / pathology*
  • Sjogren's Syndrome / diagnosis*
  • Sjogren's Syndrome / pathology*

Substances

  • Immunoglobulin M
  • Bence Jones Protein