Abstract
We report a complex and rare combination of clinical and histological findings in a 59-year-old female patient: severe sicca-syndrome due to M. Sjögren, marginal zone B-cell lymphoma (MALT-type) in labial salivary glands with localized amyloid deposition, IgM-paraproteinemia, and Bence-Jones proteinuria. The causal association of these findings could only be elucidated by intense interdisciplinary correlation of all findings.
Publication types
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Case Reports
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English Abstract
MeSH terms
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Amyloidosis / diagnosis*
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Amyloidosis / pathology*
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Bence Jones Protein / analysis
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Biopsy
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Cooperative Behavior
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Female
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Humans
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Immunoglobulin M / analysis*
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Interdisciplinary Communication
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Lip Diseases / diagnosis*
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Lip Diseases / pathology*
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Lip Neoplasms / diagnosis*
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Lip Neoplasms / pathology*
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Lip Neoplasms / surgery
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Lymphoma, B-Cell, Marginal Zone / diagnosis*
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Lymphoma, B-Cell, Marginal Zone / pathology*
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Magnetic Resonance Imaging
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Melanoma / surgery
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Middle Aged
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Neoplasms, Multiple Primary / surgery
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Paraproteinemias / diagnosis*
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Paraproteinemias / pathology*
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Patient Care Team
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Postoperative Complications / diagnosis
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Postoperative Complications / pathology
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Salivary Gland Neoplasms / diagnosis*
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Salivary Gland Neoplasms / pathology*
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Salivary Glands, Minor / pathology*
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Sjogren's Syndrome / diagnosis*
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Sjogren's Syndrome / pathology*
Substances
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Immunoglobulin M
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Bence Jones Protein