Early infantile epileptic encephalopathy with unusual favourable outcome

Brain Dev. 2010 Sep;32(8):673-6. doi: 10.1016/j.braindev.2009.08.007. Epub 2009 Sep 19.

Abstract

The authors report the case of an infant suffered from early infantile epileptic encephalopathy with suppression-burst, or Ohtahara syndrome, a severe form of epilepsy in early childhood. The patient was treated with vigabatrin causing a favourable response. This unusual outcome may be related with the normality of neuroimaging and metabolic studies, as happens with idiopathic West syndrome cases.

Publication types

  • Case Reports

MeSH terms

  • Anticonvulsants / therapeutic use*
  • Brain Diseases* / drug therapy
  • Brain Diseases* / physiopathology
  • Electroencephalography
  • Epilepsy* / drug therapy
  • Epilepsy* / physiopathology
  • Female
  • Humans
  • Infant
  • Male
  • Pregnancy
  • Spasms, Infantile / physiopathology
  • Syndrome
  • Treatment Outcome
  • Vigabatrin / therapeutic use*

Substances

  • Anticonvulsants
  • Vigabatrin