Abstract
An adolescent with idiopathic CD4 lymphocytopenia suffered from 4 visceral leishmaniasis relapses despite appropriate treatment. CD8 lymphocytopenia and abnormal expansion of TCRalphabeta, CD4, CD8 cells were consistently detected together with reduced export of mature T cells from thymus. This novel form of idiopathic CD4 lymphocytopenia may predispose to multiple visceral leishmaniasis relapses.
Publication types
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Case Reports
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Research Support, Non-U.S. Gov't
MeSH terms
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Adolescent
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Allopurinol / therapeutic use
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Amphotericin B / therapeutic use
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Antipruritics / therapeutic use
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Female
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Humans
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Immunophenotyping
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Keratins / metabolism
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Leishmaniasis, Visceral / complications*
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Leishmaniasis, Visceral / drug therapy
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Leishmaniasis, Visceral / immunology
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Lymph Nodes / pathology
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Recurrence
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T-Lymphocytopenia, Idiopathic CD4-Positive / complications*
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T-Lymphocytopenia, Idiopathic CD4-Positive / immunology
Substances
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Antipruritics
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liposomal amphotericin B
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Allopurinol
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Keratins
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Amphotericin B