[Devic disease associated with isolated spinal cord atrophy]

Rev Neurol (Paris). 2007 Dec;163(12):1236-8. doi: 10.1016/S0035-3787(07)78409-6.
[Article in French]

Abstract

Devic disease is a rare entity characterized by bilateral optic neuritis and transverse myelitis. Recently, recognition of antibody activity (Anti NMO) led to broaden the clinical and MR phenotype spectrum of this disease. This report is about a patient with spinal cord atrophy and bilateral optic neuritis, occurring more than 8 years after symptom onset.

Publication types

  • Case Reports
  • English Abstract

MeSH terms

  • Adult
  • Atrophy
  • Autoantibodies / analysis
  • Electromyography
  • Humans
  • Magnetic Resonance Imaging
  • Male
  • Neurologic Examination
  • Neuromyelitis Optica / complications*
  • Neuromyelitis Optica / pathology
  • Phenotype
  • Spinal Cord / pathology*
  • Spinal Cord Diseases / complications*
  • Spinal Cord Diseases / pathology*

Substances

  • Autoantibodies