A case of congenital peripheral primitive neuroectodermal tumor presenting with multiple metastases

J Pediatr Hematol Oncol. 2008 Jan;30(1):36-8. doi: 10.1097/MPH.0b013e31815cf730.

Abstract

The report describes a case of a newborn with a huge congenital abdominal peripheral primitive neuroectodermal tumor, with peritoneal dissemination and cutaneous involvement, and discusses literature data. Peripheral primitive neuroectodermal tumor is an exceedingly uncommon tumor in this age group and is characterized by very aggressive behavior and poor prognosis.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Adult
  • Fatal Outcome
  • Female
  • Humans
  • Infant, Newborn
  • Infant, Newborn, Diseases / drug therapy
  • Infant, Newborn, Diseases / metabolism
  • Infant, Newborn, Diseases / pathology*
  • Neuroectodermal Tumors, Primitive, Peripheral / congenital
  • Neuroectodermal Tumors, Primitive, Peripheral / drug therapy
  • Neuroectodermal Tumors, Primitive, Peripheral / metabolism
  • Neuroectodermal Tumors, Primitive, Peripheral / pathology*
  • Peritoneal Neoplasms / congenital
  • Peritoneal Neoplasms / drug therapy
  • Peritoneal Neoplasms / metabolism
  • Peritoneal Neoplasms / pathology*
  • Skin Neoplasms / congenital
  • Skin Neoplasms / drug therapy
  • Skin Neoplasms / metabolism
  • Skin Neoplasms / pathology*