Octanoate and palmitate beta-oxidation in human leukocytes: implications for the rapid diagnosis of fatty acid beta-oxidation disorders

J Inherit Metab Dis. 1991;14(3):317-20. doi: 10.1007/BF01811692.
No abstract available

Publication types

  • Case Reports

MeSH terms

  • Acyl-CoA Dehydrogenase
  • Acyl-CoA Dehydrogenase, Long-Chain
  • Caprylates / metabolism*
  • Fatty Acid Desaturases / deficiency
  • Fatty Acids / metabolism*
  • Fibroblasts / enzymology
  • Humans
  • In Vitro Techniques
  • Infant
  • Leukocytes / metabolism*
  • Lipid Metabolism, Inborn Errors / diagnosis*
  • Oxidation-Reduction
  • Palmitic Acid
  • Palmitic Acids / metabolism*

Substances

  • Caprylates
  • Fatty Acids
  • Palmitic Acids
  • Palmitic Acid
  • Fatty Acid Desaturases
  • Acyl-CoA Dehydrogenase
  • Acyl-CoA Dehydrogenase, Long-Chain
  • octanoic acid