Left atrium myxosarcoma: an exceptional cardiac malignant primary tumor

Clin Cardiol. 2007 Jun;30(6):306-8. doi: 10.1002/clc.20045.

Abstract

We report the case of a 32-year-old patient with a left atrium myxosarcoma, presenting with congestive heart failure. It is a rare cardiac malignant primary tumor that seems to derive from the same cellular line as myxomas, but the prognosis is very different. These tumors present local recidives and distance metastasis, so the mean survival is about 1 year, independent of any therapeutical option.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Diagnosis, Differential
  • Echocardiography, Transesophageal
  • Fatal Outcome
  • Heart Atria / diagnostic imaging
  • Heart Atria / pathology
  • Heart Failure / diagnostic imaging
  • Heart Failure / etiology*
  • Heart Failure / pathology
  • Heart Neoplasms / complications
  • Heart Neoplasms / diagnosis*
  • Heart Neoplasms / diagnostic imaging
  • Heart Neoplasms / pathology
  • Heart Neoplasms / therapy
  • Humans
  • Male
  • Myxoma / diagnosis*
  • Myxosarcoma / complications
  • Myxosarcoma / diagnosis*
  • Myxosarcoma / diagnostic imaging
  • Myxosarcoma / pathology
  • Myxosarcoma / therapy
  • Neoplasm Recurrence, Local / diagnosis*
  • Prognosis