The prion protein is neuroprotective against retinal degeneration in vivo

Exp Eye Res. 2006 Dec;83(6):1350-8. doi: 10.1016/j.exer.2006.07.010. Epub 2006 Sep 6.

Abstract

A common feature of neurodegenerative disorders is acute or progressive loss of neurons due to apoptosis. The pathological isoform of the prion protein is associated with retinal apoptosis and the cellular isoform (PrPc) has been shown to mediate protection from apoptosis in cell culture and in neonatal retinal explants. Using a model of light-induced photoreceptor apoptosis, we show in vivo that the levels of PrPc expression in the retina inversely correlate with the susceptibility of photoreceptors to light damage. Dissection of apoptotic signalling cascades suggests that PrPc acts neuroprotectively downstream of AP-1 induction. Our results reveal PrP as a neuroprotective/anti-apoptotic factor in vivo and suggest that PrPc may function as a guardian of neuronal integrity.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Apoptosis / radiation effects
  • Disease Susceptibility
  • Electrophoretic Mobility Shift Assay
  • Light
  • Mice
  • Mice, Inbred BALB C
  • Photoreceptor Cells, Vertebrate / radiation effects
  • PrPC Proteins / metabolism
  • PrPC Proteins / physiology*
  • Radiation Injuries, Experimental / metabolism
  • Radiation Injuries, Experimental / pathology
  • Radiation Injuries, Experimental / prevention & control
  • Retina / metabolism
  • Retinal Degeneration / metabolism
  • Retinal Degeneration / pathology
  • Retinal Degeneration / prevention & control*
  • Signal Transduction / radiation effects

Substances

  • PrPC Proteins