A modification of De Leval technique for closure of ventricular septal defect (VSD) in atrioventricular discordance (AVD) with double outlet right ventricle (DORV) was reported. A 2-year-and-8-month-old boy underwent total repair for this anomaly. The first two stitches for closure of VSD were placed on the lower margin of the defect in which conducting tissues were not situated. Next remained stitches for closure of the defect could be continued toward upper margin of VSD in the morphologically right ventricular side of VSD while pulling the just previous stitches with good exposure and ease. We concluded that this modification was useful for making safe De Leval technique for closure of VSD in AVD.