Background: Primary ovarian leiomyoma is a very rare tumor and usually it is small, unilateral-, and concomitantly seen with uterine leiomyomata in middle-aged to postmenopausal women.
Case: We describe a case of huge, bilateral ovarian leiomyoma that was not associated with uterine tumor in a 17-year-old woman. The authors of this study documented the smooth muscle origin of the tumor with immunohistochemical studies, the available literature was reviewed and the possible histogenesis was discussed.
Conclusion: We herein report a case of a rare primary bilateral ovarian leiomyoma in a young woman.