A 20-year-old female patient with familial adenomatous polyposis diagnosed on the occasion of the screening of her family, which had a history of three deaths due malignant colic polyposis, was submitted to total colectomy by laparoscopic technique. Though the histopathological examination performed on two polypi excised by endoscopic technique did not evidence signs of malignant shift, total colectomy was performed, observing the oncological principles. The intervention was uneventful and postoperative course uncomplicated, the patient being socially reintegrated after three weeks. Follow-up examinations performed up to 18 months after the operation showed a favourable evolution and no development in the size and number of polypi.