Tracheobronchial stent insertions in the management of major airway obstruction in a patient with Hunter syndrome (type-II mucopolysaccharidosis)

Eur Radiol. 2002 Feb;12(2):458-62. doi: 10.1007/s003300100932. Epub 2001 Jun 19.

Abstract

We report a case of a 22-year-old male with Hunter syndrome who developed progressive major airway obstruction and was treated with insertion of plastic and metallic stents, with dramatic improvement in the patient's symptomatic and functional status. To the best of our knowledge, this is the first reported case of endoluminal stents being used in the management of major airway obstruction in a patient with Hunter syndrome.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Catheterization
  • Humans
  • Lung Diseases, Obstructive / etiology*
  • Lung Diseases, Obstructive / therapy*
  • Male
  • Mucopolysaccharidosis II / complications*
  • Recurrence
  • Stents*
  • Tracheal Stenosis / etiology
  • Tracheal Stenosis / therapy