[An acceptor-splice-site mutation responsible for complete androgen insensitivity syndrome]

Zhonghua Yi Xue Yi Chuan Xue Za Zhi. 2001 Feb;18(1):14-6.
[Article in Chinese]

Abstract

Objective: To study the molecular mechanism of androgen insensitivity syndrome (AIS) and the relationship among androgen receptor's molecular structure, function and clinical manifestation.

Methods: PCR-SSCP analysis was carried out to screen exons from B to H of androgen receptor(AR) gene in a cAIS patient for AR gene mutation; direct DNA sequencing of PCR product was performed to find out the location and the pattern of the mutation.

Results: A newly found point mutation G(3346) to T, which is located at intron 5-exon F acceptor splice site in the AR gene, was identified.

Conclusion: Highly conserved GU-AG structure at splice site plays a crucial role in maintaining normal function of AR.

Publication types

  • Case Reports
  • English Abstract

MeSH terms

  • Adult
  • Androgen-Insensitivity Syndrome / genetics*
  • Humans
  • Male
  • Point Mutation*
  • Polymerase Chain Reaction
  • Polymorphism, Single-Stranded Conformational
  • Receptors, Androgen / genetics*

Substances

  • Receptors, Androgen