Expanding our understanding of polyglutamine diseases through mouse models

Neuron. 1999 Nov;24(3):499-502. doi: 10.1016/s0896-6273(00)81104-6.
No abstract available

Publication types

  • Review

MeSH terms

  • Animals
  • Cell Nucleus / ultrastructure
  • Disease Models, Animal
  • Inclusion Bodies / ultrastructure
  • Mice
  • Mutation / physiology
  • Neurodegenerative Diseases / genetics
  • Neurodegenerative Diseases / metabolism*
  • Neurodegenerative Diseases / pathology*
  • Peptides / chemistry
  • Peptides / genetics
  • Peptides / metabolism*

Substances

  • Peptides
  • polyglutamine